General Information of the Protein
Protein ID
PT06578
Protein Name
Ferrochelatase, mitochondrial
Secondarily
Protein Name
Heme synthase
Protoheme ferro-lyase
Gene Name
FECH
Sequence
MRSLGANMAAALRAAGVLLRDPLASSSWRVCQPWRWKSGAAAAAVTTETAQHAQGAKPQVQPQKRKPKTGILMLNMGGPETLGDVHDFLLRLFLDRDLMTLPIQNKLAPFIAKRRTPKIQEQYRRIGGGSPIKIWTSKQGEGMVKLLDELSPNTAPHKYYIGFRYVHPLTEEAIEEMERDGLERAIAFTQYPQYSCSTTGSSLNAIYRYYNQVGRKPTMKWSTIDRWPTHHLLIQCFADHILKELDHFPLEKRSEVVILFSAHSLPMSVVNRGDPYPQEVSATVQKVMERLEYCNPYRLVWQSKVGPMPWLGPQTDESIKGLCERGRKNILLVPIAFTSDHIETLYELDIEYSQVLAKECGVENIRRAESLNGNPLFSKALADLVHSHIQSNELCSKQLTLSCPLCVNPVCRETKSFFTSQQL
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Organism
Homo sapiens, Human
Protein Classification
Enzyme
>
Lyase
Function
Catalyzes the ferrous insertion into protoporphyrin IX.
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Uniprot ID
Primary ID:
P22830

Secondarily ID:
A8KA72
Q8IXN1
Q8NAN0
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Ensembl ID
ENSG00000066926
HGNC ID
HGNC:3647
Subcellular Location
Mitochondrion inner membrane
Clinical Information about the Protein
Target 1 ( Ferrochelatase (FECH) )
Target Type Successful Target
Disease 1 Target-related Disease  1
1 Synthesis disorder [ICD-11: 5C52-5C59]
Approved Drug(s) 1 Approved Drug  1
1 Cholic Acid Approved
Synthesis disorder